Template:ICD-10-circulatory system Q20-Q28 table

From Embryology
ICD10 Congenital malformations of the circulatory system (Q20-Q28)  
Cardiovascular System - Abnormalities
Q20 Congenital malformations of cardiac chambers and connections

Excl.: dextrocardia with situs inversus (Q89.3) mirror-image atrial arrangement with situs inversus (Q89.3)

  • Q20.0 Common arterial trunk Persistent truncus arteriosus
  • Q20.1 Double outlet right ventricle Taussig-Bing syndrome
  • Q20.2 Double outlet left ventricle
  • Q20.3 Discordant ventriculoarterial connection Dextrotransposition of aorta Transposition of great vessels (complete)
  • Q20.4 Double inlet ventricle Common ventricle Cor triloculare biatriatum Single ventricle
  • Q20.5 Discordant atrioventricular connection Corrected transposition Laevotransposition Ventricular inversion
  • Q20.6 Isomerism of atrial appendages Isomerism of atrial appendages with asplenia or polysplenia
  • Q20.8 Other congenital malformations of cardiac chambers and connections
  • Q20.9 Congenital malformation of cardiac chambers and connections, unspecified
Q21 Congenital malformations of cardiac septa

Excl.: acquired cardiac septal defect (I51.0)

  • Q21.0 Ventricular septal defect
  • Q21.1 Atrial septal defect Coronary sinus defect Patent or persistent: foramen ovale ostium secundum defect (type II) Sinus venosus defect
  • Q21.2 Atrioventricular septal defect Common atrioventricular canal Endocardial cushion defect Ostium primum atrial septal defect (type I)
  • Q21.3 Tetralogy of Fallot Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
  • Q21.4 Aortopulmonary septal defect Aortic septal defect Aortopulmonary window
  • Q21.8 Other congenital malformations of cardiac septa Eisenmenger's defect Pentalogy of Fallot Excl.: Eisenmenger's complex (I27.8) syndrome (I27.8)
  • Q21.9 Congenital malformation of cardiac septum, unspecified Septal (heart) defect NOS
Q22 Congenital malformations of pulmonary and tricuspid valves
  • Q22.0 Pulmonary valve atresia
  • Q22.1 Congenital pulmonary valve stenosis
  • Q22.2 Congenital pulmonary valve insufficiency Congenital pulmonary valve regurgitation
  • Q22.3 Other congenital malformations of pulmonary valve Congenital malformation of pulmonary valve NOS
  • Q22.4 Congenital tricuspid stenosis Tricuspid atresia
  • Q22.5 Ebstein's anomaly
  • Q22.6 Hypoplastic right heart syndrome
  • Q22.8 Other congenital malformations of tricuspid valve
  • Q22.9 Congenital malformation of tricuspid valve, unspecified
Q23 Congenital malformations of aortic and mitral valves
  • Q23.0 Congenital stenosis of aortic valve Congenital aortic: atresia stenosis Excl.: congenital subaortic stenosis (Q24.4) that in hypoplastic left heart syndrome (Q23.4)
  • Q23.1 Congenital insufficiency of aortic valve Bicuspid aortic valve Congenital aortic insufficiency
  • Q23.2 Congenital mitral stenosis Congenital mitral atresia
  • Q23.3 Congenital mitral insufficiency
  • Q23.4 Hypoplastic left heart syndrome Atresia, or marked hypoplasia of aortic orifice or valve, with hypoplasia of ascending aorta and defective develop-ment of left ventricle (with mitral valve stenosis or atresia).
  • Q23.8 Other congenital malformations of aortic and mitral valves
  • Q23.9 Congenital malformation of aortic and mitral valves, unspecified
Q24 Other congenital malformations of heart

Excl.: endocardial fibroelastosis (I42.4)

  • Q24.0 Dextrocardia Excl.: dextrocardia with situs inversus (Q89.3) isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6) mirror-image atrial arrangement with situs inversus (Q89.3)
  • Q24.1 Laevocardia Location of heart in left hemithorax with apex pointing to the left, but with situs inversus of other viscera and defects of the heart, or corrected transposition of great vessels.
  • Q24.2 Cor triatriatum
  • Q24.3 Pulmonary infundibular stenosis
  • Q24.4 Congenital subaortic stenosis
  • Q24.5 Malformation of coronary vessels Congenital coronary (artery) aneurysm
  • Q24.6 Congenital heart block
  • Q24.8 Other specified congenital malformations of heart Congenital: diverticulum of left ventricle malformation of: myocardium pericardium Malposition of heart Uhl's disease
  • Q24.9 Congenital malformation of heart, unspecified Congenital: anomaly disease NOS of heart
Q25 Congenital malformations of great arteries
  • Q25.0 Patent ductus arteriosus Patent ductus Botallo Persistent ductus arteriosus
  • Q25.1 Coarctation of aorta Coarctation of aorta (preductal)(postductal)
  • Q25.2 Atresia of aorta
  • Q25.3 Stenosis of aorta Supravalvular aortic stenosis Excl.: congenital aortic stenosis (Q23.0)
  • Q25.4 Other congenital malformations of aorta Absence Aplasia Congenital: aneurysm dilatation of aorta Aneurysm of sinus of Valsalva (ruptured) Double aortic arch [vascular ring of aorta] Hypoplasia of aorta Persistent: convolutions of aortic arch right aortic arch Excl.: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)
  • Q25.5 Atresia of pulmonary artery
  • Q25.6 Stenosis of pulmonary artery Supravalvular pulmonary stenosis
  • Q25.7 Other congenital malformations of pulmonary artery Aberrant pulmonary artery Agenesis Aneurysm, congenital Anomaly Hypoplasia of pulmonary artery Pulmonary arteriovenous aneurysm
  • Q25.8 Other congenital malformations of great arteries
  • Q25.9 Congenital malformation of great arteries, unspecified
Q26 Congenital malformations of great veins
  • Q26.0 Congenital stenosis of vena cava Congenital stenosis of vena cava (inferior)(superior)
  • Q26.1 Persistent left superior vena cava
  • Q26.2 Total anomalous pulmonary venous connection
  • Q26.3 Partial anomalous pulmonary venous connection
  • Q26.4 Anomalous pulmonary venous connection, unspecified
  • Q26.5 Anomalous portal venous connection
  • Q26.6 Portal vein-hepatic artery fistula
  • Q26.8 Other congenital malformations of great veins Absence of vena cava (inferior)(superior) Azygos continuation of inferior vena cava Persistent left posterior cardinal vein Scimitar syndrome
  • Q26.9 Congenital malformation of great vein, unspecified Anomaly of vena cava (inferior)(superior) NOS
Q27 Other congenital malformations of peripheral vascular system

Excl.: anomalies of: cerebral and precerebral vessels (Q28.0-Q28.3) coronary vessels (Q24.5) pulmonary artery (Q25.5-Q25.7) congenital retinal aneurysm (Q14.1) haemangioma and lymphangioma (D18.-)

  • Q27.0 Congenital absence and hypoplasia of umbilical artery Single umbilical artery
  • Q27.1 Congenital renal artery stenosis
  • Q27.2 Other congenital malformations of renal artery Congenital malformation of renal artery NOS Multiple renal arteries
  • Q27.3 Peripheral arteriovenous malformation Arteriovenous aneurysm Excl.: ac
  • Quired arteriovenous aneurysm (I77.0)
  • Q27.4 Congenital phlebectasia
  • Q27.8 Other specified congenital malformations of peripheral vascular system Aberrant subclavian artery Absence Atresia of artery or vein NEC Congenital: aneurysm (peripheral) stricture, artery varix
  • Q27.9 Congenital malformation of peripheral vascular system, unspecified Anomaly of artery or vein NOS
Q28 Other congenital malformations of circulatory system

Excl.: congenital aneurysm: NOS (Q27.8) coronary (Q24.5) peripheral (Q27.8) pulmonary (Q25.7) retinal (Q14.1) ruptured: cerebral arteriovenous malformation (I60.8) malformation of precerebral vessels (I72.-)

  • Q28.0 Arteriovenous malformation of precerebral vessels Congenital arteriovenous precerebral aneurysm (nonruptured)
  • Q28.1 Other malformations of precerebral vessels Congenital: malformation of precerebral vessels NOS precerebral aneurysm (nonruptured)
  • Q28.2 Arteriovenous malformation of cerebral vessels Arteriovenous malformation of brain NOS Congenital arteriovenous cerebral aneurysm (nonruptured)
  • Q28.3 Other malformations of cerebral vessels Congenital: cerebral aneurysm (nonruptured) malformation of cerebral vessels NOS
  • Q28.8 Other specified congenital malformations of circulatory system Congenital aneurysm, specified site NEC
  • Q28.9 Congenital malformation of circulatory system, unspecified