Cardiovascular System - Coarctation of the Aorta: Difference between revisions

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Embryology - 19 Apr 2024 Expand to Translate
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ICD-11

LA8B.21 Coarctation of aorta

A congenital cardiovascular malformation in which there is a discrete luminal narrowing of the junction between the aortic arch and the descending aorta. Coarctation of the aorta generally indicates a narrowing of the descending thoracic aorta just distal to the left subclavian artery. However, the term may also be accurately used to refer to a region of narrowing anywhere in the thoracic or abdominal aorta.

LA8B.22 Interrupted aortic arch

ICD-11 Structural developmental anomalies of the circulatory system (draft)
ICD-11 Beta Draft - NOT FINAL, updated on a daily basis, It is not approved by WHO, NOT TO BE USED for CODING except for agreed FIELD TRIALS. 20 Developmental Anomalies - Structural Developmental Anomalies Beta coding and tree structure for "structural developmental anomalies" within this section are shown in the table below.
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart and great vessels LB00 Congenital heart or great vessel related acquired abnormality LB01 Congenital anomaly of atrioventricular or ventriculo-arterial connections LB01.1 Transposition of the great arteries LB01.2 Double outlet right ventricle LB01.3 Double outlet left ventricle LB01.4 Common arterial trunk LB01.Y Other specified congenital anomaly of atrioventricular or ventriculo-arterial connections LB01.Z Congenital anomaly of atrioventricular or ventriculo-arterial connections, unspecified LB02 Congenital anomaly of the mediastinal veins Congenital anomaly of atria or atrial septum LB20 Congenital anomaly of atrioventricular valves or septum LB21 Congenital anomaly of ventricles and ventricular septum LB21.1 Congenital right ventricular outflow tract obstruction LB21.2 Double-chambered right ventricle LB21.3 Tetralogy of Fallot LB21.4 Congenital left ventricular outflow tract obstruction LB21.5 Congenital ventricular septal defects LB21.Y Other specified congenital anomaly of ventricles and ventricular septum LB21.Z Congenital anomaly of ventricles and ventricular septum, unspecified LB22 Functionally univentricular heart LB23 Congenital anomaly of ventriculo-arterial valves and adjacent regions LB24 Congenital anomaly of great arteries including arterial duct LB.1 Congenital aorto-pulmonary window LB.2 Congenital anomaly of pulmonary arterial tree LB.3 Congenital anomaly of aorta and its branches LB.4 Tracheo-oesophageal compressive syndrome LB.5 Patent arterial duct LB.Y Other specified congenital anomaly of great arteries including arterial duct LB.Z Congenital anomaly of great arteries including arterial duct, unspecified LB25 Anomalous position-orientation of heart LB26 Total mirror imagery LB27 Left isomerism LB28 Congenital anomaly of coronary arteries LB29 Structural developmental anomalies of the pericardium LB2Y Other specified structural developmental anomaly of heart and great vessels LB2Z Structural developmental anomaly of heart and great vessels, unspecified LB30 Structural developmental anomalies of the peripheral vascular system LB30.1 Capillary malformations LB30.2 Lymphatic malformations LB30.21 Macrocystic lymphatic malformation LB30.22 Microcystic lymphatic malformation LB30.23 Cystic hygroma in fetus BD23.1 Primary lymphoedema EK91 Yellow nail syndrome LC5F.26 Noonan syndrome LB30.2Y Other specified lymphatic malformations LB30.2Z Lymphatic malformations, unspecified LB30.3 Peripheral venous malformations LB30.4 Peripheral arteriovenous malformations LB30.5 Peripheral arterial malformations LB30.6 Pulmonary arteriovenous fistula LB30.Y Other specified structural developmental anomalies of the peripheral vascular system LB30.Z Structural developmental anomalies of the peripheral vascular system, unspecified LB3Y Other specified structural developmental anomalies of the circulatory system LB3Z Structural developmental anomalies of the circulatory system, unspecified
CD-11 Beta Draft - NOT FINAL, updated on a daily basis, It is not approved by WHO, NOT TO BE USED for CODING except for agreed FIELD TRIALS. See also International Classification of Diseases \| Abnormalities

Introduction

Coarctation of the Aorta

5-8% of Congenital Heart Disease
Aortic constriction.
Treatment aims at maintaining the ductus arteriosus via prostaglandins and by surgical intervention.
Recent review^[1] suggests it may:
- affect the aortic arch in a highly variable manner
- be associated with a host of other left sided heart lesions
- represent a wider vasculopathy within the pre-coarctation arterial tree

Links: Search PubMed | PMID 21947983 | 2011 Review PDF

Some Recent Findings

Multicenter experience with endovascular treatment of aortic coarctation in adults^[2] "The objective of this study was to evaluate outcomes of endovascular treatment of aortic coarctation in adults. Clinical data and imaging studies of 93 consecutive patients treated at nine institutions from 1999 to 2015 were reviewed. We included newly diagnosed aortic coarctation (NCO), recurrent coarctation, and aneurysmal/pseudoaneurysmal degeneration (ANE) after prior open surgical repair (OSR) of coarctation. Primary end points were morbidity and mortality. Secondary end points were stent patency and freedom from reintervention. Endovascular repair is effective with an acceptable safety profile in the treatment of NCO and postsurgical complications of coarctation after initial OSR. Aortic rupture is an infrequent (2%) but devastating complication with high mortality. Balloon-expandable covered stents are preferred for NCO, whereas stent grafts are used for ANE. The rate of reinterventions is acceptable, with high procedural and long-term clinical success."

More recent papers
This table allows an automated computer search of the external PubMed database using the listed "Search term" text link. This search now requires a manual link as the original PubMed extension has been disabled. The displayed list of references do not reflect any editorial selection of material based on content or relevance. References also appear on this list based upon the date of the actual page viewing. References listed on the rest of the content page and the associated discussion page (listed under the publication year sub-headings) do include some editorial selection based upon both relevance and availability. More? References \| Discussion Page \| Journal Searches \| 2019 References \| 2020 References Search term: Coarctation of the Aorta

Older papers
These papers originally appeared in the Some Recent Findings table, but as that list grew in length have now been shuffled down to this collapsible table. See also the Discussion Page for other references listed by year and References on this current page.

Sex Ratios

**USA Abnormalities Sex Ratio (1997-2009)**
Male preponderance	Female preponderance
craniosynostosis (2.12) cleft lip and palate (2.01) cleft lip without cleft palate (1.78)	choanal atresia (0.45) cloacal exstrophy (0.46) holoprosencephaly (0.64)
Cardiac defects
aortic stenosis (2.88) coarctation of the aorta (2.51) transposition of the great vessels (2.34)	multiple ventricular septal defects (0.52) truncus arteriosus (0.63) heterotaxia with congenital heart defect (0.64)
Table data^[3] Links: abnormal development \| cardiovascular abnormalities \| USA \| Male \| Female \| cleft lip and palate

Ultrasound

Echocardiography uses standard two-dimensional, three-dimensional, and Doppler ultrasound to create images of the heart.

Echocardiogram Coarctation of the Aorta^[4]

A Two-dimensional transthoracic echocardiogram image obtained from the suprasternal notch in an 11-day-old infant demonstrating discrete coarctation (arrow).	B Colour Doppler of the same image with aliasing of flow at the site of coarctation (arrow).

References

↑ Kenny D & Hijazi ZM. (2011). Coarctation of the aorta: from fetal life to adulthood. Cardiol J , 18, 487-95. PMID: 21947983
↑ Erben Y, Oderich GS, Verhagen HJM, Witsenburg M, van den Hoven AT, Debus ES, Kölbel T, Arko FR, Torsello GB, Torsello GF, Lawrence PF, Harlander-Locke MP, Bacharach JM, Jordan WD, Eskandari MK & Hagler DJ. (2019). Multicenter experience with endovascular treatment of aortic coarctation in adults. J. Vasc. Surg. , 69, 671-679.e1. PMID: 30528403 DOI.
↑ Michalski AM, Richardson SD, Browne ML, Carmichael SL, Canfield MA, VanZutphen AR, Anderka MT, Marshall EG & Druschel CM. (2015). Sex ratios among infants with birth defects, National Birth Defects Prevention Study, 1997-2009. Am. J. Med. Genet. A , 167A, 1071-81. PMID: 25711982 DOI.
↑ Torok RD, Campbell MJ, Fleming GA & Hill KD. (2015). Coarctation of the aorta: Management from infancy to adulthood. World J Cardiol , 7, 765-75. PMID: 26635924 DOI.

Reviews

Articles

Search Pubmed

Search Pubmed: Coarctation of the Aorta

Search OMIM: Coarctation of the Aorta

External Links

External Links Notice - The dynamic nature of the internet may mean that some of these listed links may no longer function. If the link no longer works search the web with the link text or name. Links to any external commercial sites are provided for information purposes only and should never be considered an endorsement. UNSW Embryology is provided as an educational resource with no clinical information or commercial affiliation.

MedlinePlus Patent Ductus Arteriosus
OMIM 607411 Patent Ductus Arteriosus

Glossary Links

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Cite this page: Hill, M.A. (2024, April 19) Embryology Cardiovascular System - Coarctation of the Aorta. Retrieved from https://embryology.med.unsw.edu.au/embryology/index.php/Cardiovascular_System_-_Coarctation_of_the_Aorta

What Links Here?

[PMID21947983-1] Kenny D & Hijazi ZM. (2011). Coarctation of the aorta: from fetal life to adulthood. Cardiol J , 18, 487-95. PMID: 21947983

[PMID30528403-2] Erben Y, Oderich GS, Verhagen HJM, Witsenburg M, van den Hoven AT, Debus ES, Kölbel T, Arko FR, Torsello GB, Torsello GF, Lawrence PF, Harlander-Locke MP, Bacharach JM, Jordan WD, Eskandari MK & Hagler DJ. (2019). Multicenter experience with endovascular treatment of aortic coarctation in adults. J. Vasc. Surg. , 69, 671-679.e1. PMID: 30528403 DOI.

[PMID25711982-3] Michalski AM, Richardson SD, Browne ML, Carmichael SL, Canfield MA, VanZutphen AR, Anderka MT, Marshall EG & Druschel CM. (2015). Sex ratios among infants with birth defects, National Birth Defects Prevention Study, 1997-2009. Am. J. Med. Genet. A , 167A, 1071-81. PMID: 25711982 DOI.

[PMID26635924-4] Torok RD, Campbell MJ, Fleming GA & Hill KD. (2015). Coarctation of the aorta: Management from infancy to adulthood. World J Cardiol , 7, 765-75. PMID: 26635924 DOI.

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@@ Line 67: / Line 67: @@
 | colspan=2|[[File:Aorta coarctation echocardiogram.jpg|alt=Aorta coarctation echocardiogram]]
 |-
-| '''A''' Two-dimensional transthoracic echocardiogram image obtained from the suprasternal notch in an 11-day-old infant demonstrating discrete coarctation (arrow);
+| width=300px|'''A''' Two-dimensional transthoracic echocardiogram image obtained from the suprasternal notch in an 11-day-old infant demonstrating discrete coarctation (arrow).
-| '''B''' Colour Doppler of the same image with aliasing of flow at the site of coarctation (arrow).
+| width=300px|'''B''' Colour Doppler of the same image with aliasing of flow at the site of coarctation (arrow).
 |}