Abnormal Development - Congenital Hydrocephalus
Q03 Congenital hydrocephalus
International Classification of Diseases
Incl.: hydrocephalus in newborn Excl.: Arnold-Chiari syndrome (Q07.0) hydrocephalus: acquired (G91.-) due to congenital toxoplasmosis (P37.1) with spina bifida (Q05.0-Q05.4)
- Q03.0 Malformations of aqueduct of Sylvius Aqueduct of Sylvius: anomaly obstruction, congenital stenosis
- Q03.1 Atresia of foramina of Magendie and Luschka Dandy-Walker syndrome
- Q03.8 Other congenital hydrocephalus
- Q03.9 Congenital hydrocephalus, unspecified
This is a defect of cerebrospinal fliud (CSF) flow, excess fluid production or impaired fluid absorption and can be congenital or acquired. Estimated incidence of 1 in 1000 live births the condition leads to enlarged ventricles and head, separated skull cranial sutures and fontanelles. Obstruction of CSF flow can occur at any time (prenatally or postnatally) and leads to accumulation of within the ventricles. The time of onset will have different effects and should be compared to the equilivant neurological events that are occuring.
Ventricular obstruction usually occurs at the level of the cerebral aqueduct (narrowest site), but can occur elsewhere, and can be caused by viral infection or zoonotic disease.
Some Recent Findings
ICD - Q07 Other congenital malformations of nervous system - Q07.0 Arnold-Chiari syndrome
Magnetic Resonance Image Sagittal T1-weighted image showing Chiari II malformation.
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Cite this page: Hill, M.A. (2021, December 1) Embryology Abnormal Development - Congenital Hydrocephalus. Retrieved from https://embryology.med.unsw.edu.au/embryology/index.php/Abnormal_Development_-_Congenital_Hydrocephalus
- © Dr Mark Hill 2021, UNSW Embryology ISBN: 978 0 7334 2609 4 - UNSW CRICOS Provider Code No. 00098G